|
KMID : 0352120220370010034
|
|
Journal of Kyung Hee University
2022 Volume.37 No. 1 p.34 ~ p.38
|
|
|
General Anesthesia of a Patient with Charcot-Marie-Tooth Disease
|
|
Lee Jun-Bum
Kim Ga-Hee
Lee Sang-Ho
Choi Jeong-Hyun
|
|
|
Abstract
|
|
|
|
Charcot-Marie-Tooth (CMT) disease is a hereditary motor and sensory neuropathy of the peripheral nervous system. The initial presentation is usually foot drop or muscle wasting of the distal part of the leg. The symptom eventually progresses to atrophy of respiratory muscles, vocal cord and diaphragm. CMT patients require special caution during the general anesthesia. CMT disease can cause malignant hyperthermia, respiratory insufficiency and hyperkalemia during anesthesia. This report presents a 50-year-old man who has been diagnosed CMT disease and scheduled to undergo anterior cervical discectomy and fusion to treat cervical spinal stenosis. Propofol and remifentanil were used for the total intravenous anesthesia, and rocuronium was used for muscle relaxant purpose. Several intraoperative monitoring methods were performed to proceed the anesthesia safely, and the patient was discharged without any complications 5 days after the surgery. This case report with comprehensive literature review investigates possible adverse events and special cautions during the general anesthesia of CMT patients, and discusses adequate intraoperative monitoring to avoid such problems.
|
|
|
KEYWORD
|
|
|
Charcot-Marie-Tooth disease, Total intravenous anesthesia, Malignant hyperthermia, Respiratory insufficiency, Hyperkalemia
|
|
|
FullTexts / Linksout information
|
|
|
|
|
Listed journal information
|
|
|
|